Primary Intramedullary Osteosarcoma of the Maxilla in a Pediatric Patient: A Case Report and Review of the Literature

Ali Amrollahie, Peter T Mai, Jason Portnof and Steven I Kaltman

Department of Oral and Maxillofacial Surgery, Nova Southeastern University College of Dental Medicine, USA
Nova Southeastern University College of Dental Medicine, USA

^*Correspondance to: Ali Amrollahie 

 PDF  Full Text DOI: 10.25107/2474-1647.2022

Abstract

Osteosarcomas are the most common malignant neoplasms of bone; mainly found in long bones. However, osteosarcomas can occur anywhere in the body. Osteosarcomas rarely occur in the head and neck and are even more uncommon in the maxilla. Primary osteosarcomas of the maxilla in pediatric patients is extremely uncommon, as head and neck osteosarcomas usually present in the third to fourth decades of life. Head and neck osteosarcomas usually arise secondary to radiation or chemotherapy treatment of a preexisting tumor. In this case report, a lesion was discovered upon routine radiographic and clinical exam in a pediatric dental office. Once the lesion was biopsied and the well differentiated, intramedullary osteosarcoma was confirmed histopathologically, a right hemi-maxillectomy was performed. Virtual surgical planning was based off a medical grade maxillofacial Computed Tomography (CT) scan. In operable cases, surgical resection of the tumor and surrounding tissue is the gold standard of treatment. Virtual planning allows for precise and accurate surgical margins. After the patient’s case was reviewed by the Joe DiMaggio children hospital tumor board, a consensus agreement on treatment planning deferred post-surgical systemic chemotherapy due to possible long-term complications.

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Cite the article

Amrollahie A, Mai PT, Portnof J, Kaltman SI. Primary Intramedullary Osteosarcoma of the Maxilla in a Pediatric Patient: A Case Report and Review of the Literature. Clin Surg. 2018; 3: 2022.