Long Term Follow-Up of Prenatal Diagnosed Isolated Giant Anterior Sacral Meningocele (ASM)

Enaam Raboei, Alaa Ghallab, Ameen Al Saggaf, Ali Zein Elabdeen and Yazeed Owiwi

Department of Pediatric Surgery, King Fahad Armed Forces Hospital, Saudi Arabia

^*Correspondance to: Enaam Raboei 

 PDF  Full Text DOI: 10.25107/2474-1647.1355

Abstract

Background: ASM is a rare congenital disorder. Usually it presents sporadically. A review of literatures indicates that no neurological consequence in comparison to posterior meningomyelocele (PMM). We present a case of ASM diagnosed prenatally and followed up for 14 years. To our knowledge this is the first published case of ASM which developed ESRD from neurogenic bladder. Management course and review of the available literatures on the disease will be presented.Method: Fetal pre sacral cyst was diagnosed in a 46 years old mother. A normal 3 kg baby girl with isolated giant ASM was followed up post natally, laparotomy and surgical removal of the sac through anterior abdominal approach was done. MRI lumbo-sacral spine was carried out for 16 available family members.Results: The family screening was negative. Generally good surgical outcome. Our patient ended with ESRD on hemodialysis with long term follow up for 14years.Conclusions: Surgical management of ASM through anterior abdominal approach is safe in immediate post natal period. The isolated ASM is sporadic and the family screening is not needed. Neurogenic bladder should be addressed with long term follow up of such cases. Treating physicians should take care of bladder dysfunction especially if the patient started to have urinary incontinence.

Keywords

ASM; Giant; Anterior; Neurogenic bladder; Sacral; Meningocele; Inheritance

Cite the article

Raboei E, Ghallab A, Al Saggaf A, Elabdeen AZ, Owiwi Y. Long Term Follow-Up of Prenatal Diagnosed Isolated Giant Anterior Sacral Meningocele (ASM). Clin Surg. 2017; 2: 1355.