Undifferentiated Embryonal Sarcoma, a Rare Liver Tumor with Atypical Presentation in an Adult: First Case Reported in Mexico

Flores Maciel KC1*, Flores Cardoza JA2, Sandoval Alvarado JJ2

1Department of General Surgery, Instituto Mexicano del Seguro Social, Unidad Médica De Alta Especialidad Hospital De Gineco Obstetricia Centro Médico Nacional De Occidente, Mexico
2Division of Liver Transplantation, Instituto Mexicano del Seguro Social, Unidad Médica De Alta Especialidad Hospital De Gineco Obstetricia Centro Médico Nacional De Occidente, Mexico

^*Correspondance to: Karla Carolina Flores Maciel 

 PDF  Full Text DOI: 10.25107/2474-1647.3652

Abstract

Undifferentiated Embryonal Sarcoma of the Liver (UESL) is a rare most common pediatric liver tumor, which clinically mimics a liver abscess when presenting with fever, abdominal pain, and a compatible lesion in image studies accompanied with other signs of systemic inflammatory response. There are approximately 108 reported cases in adults worldwide and this is the first reported in México. This case report describes an undifferentiated embryonal sarcoma of the liver in a 29-yearold female, who presented with abdominal pain, fever, nausea and vomiting, simulating a liver abscess, and initially treated like a liver abscess. The suspicion of a malignant tumor was made after its first surgical drainage; however, the histopathological diagnosis was not obtained until complete resection of the lesion was made without neural invasion, with vascular invasion, 20% necrosis, infiltrating edges and an intact capsule. The patient wasn’t candidate for chemotherapy due to her functional status. The optimal treatment approach of these neoplasms is not well defined, amongst patients who undergo surgery the indications for resection versus transplantation are not defined. Moreover, the benefit of adjuvant treatment remains questionable with existing literature reporting minimal if any benefit. The prognosis of patients with this tumor is poor, and rarely survival beyond 2 years. Nevertheless, our patient remains asymptomatic and whit no signs of recurrence after eleven months of resection.

Keywords

Undifferentiated embryonal sarcoma of the liver; Liver sarcoma; Malignant hepatic tumor; Liver; Sarcoma

Cite the article

Flores Maciel KC, Flores Cardoza JA, Sandoval Alvarado JJ. Undifferentiated Embryonal Sarcoma, a Rare Liver Tumor with Atypical Presentation in an Adult: First Case Reported in Mexico. Clin Surg. 2023; 8: 3652..