Optic Nerve Compression Caused by Sphenoid Mucocele Secondary to a Fibrous Dysplasia: Case Report and Review of the Literature

Ruth Lau1*, Dennis H Céspedes T1, Anna Pellisé-Guinjoan2, Miriam González-Pena3, María Dolores Martínez-Novoa3, Francisco J Gonçalves-Ramirez1, Cristobal Perla1, Josué Avecillas- Chasin1, Joan Francesc Garcia-Fontgibell4 and Andreu Gabarrós5

1Department of Neurological Surgery, Joan XXIII University Hospital, Spain
2Department of Neurology, Joan XXIII University Hospital, Spain
3Department of Otorhinolaryngology, Joan XXIII University Hospital, Spain
4Department of Anatomopathology, Joan XXIII University Hospital, Spain
5Department of Neurological Surgery, Bellvitge University Hospital, Barcelona, Spain

^*Correspondance to: Ruth Lau 

 PDF  Full Text DOI: 10.25107/2474-1647.3275

Abstract

We present an extremely infrequent case of a patient suffering from visual acuity loss due to optic nerve compression caused by sphenoid mucocele secondary to a fibrous dysplasia. We present a 29-year-old man reporting a gradual loss of the visual acuity in the left eye during the last five days. The complete study, including MRI, revealed an extended fibrous dysplasia involving the right sphenoid and associated to a retention mucocele causing compression to the left optic nerve on its cisternal trajectory. The patient underwent a left transnasal endoscopic sphenoidotomy with abundant drainage of the mucocele by marsupialization and creation of a new drainage pathway and preservation of the epithelium. One month later, ophthalmologic examination revealed an important improvement on the visual acuity of his left eye. Fibrous dysplasia accounts for 2% to 5% of all bone tumors. Mucoceles are benign masses that may provoke serious complications due to anatomical relationships when they grow. The apparition of both conditions associated is very rare. Acknowledging the connection between the two conditions to get an accurate diagnosis is crucial. An early surgical procedure improves the functional prognosis of the patient.

Keywords

Sphenoid mucocele; Fibrous dysplasia; Optic nerve compression

Cite the article

Lau R, Dennis H Céspedes T, Pellisé-Guinjoan A, González-Pena M, Martínez-Novoa MD, Gonçalves- Ramirez FJ, et al. Optic Nerve Compression Caused by Sphenoid Mucocele Secondary to a Fibrous Dysplasia: Case Report and Review of the Literature. Clin Surg. 2021; 6: 3275..