Atypical Case of Pulmonary Lymphangioleiomyomatosis

Joseph Costa1 , Byron Thomashow2 , Mary P Rosenblatt3 and Frank D'Ovidio1*

1 Department of Surgery, Section of Thoracic Surgery, Columbia University Medical Center, USA 2 Division of Pulmonary, Allergy and Critical Care Medicine, Columbia University Medical Center, USA 3 Department of Pathology and Cell Biology, Columbia University Medical Center, USA

^*Correspondance to: Frank D'Ovidio 

 PDF  Full Text DOI: 10.25107/2474-1647.3067

Abstract

Lymphangioleiomyomatosis is a rare idiopathic disease classically occurring in young women during their reproductive years, associated with diffuse bilateral cystic lung destruction and extrapulmonary manifestations consisting of large cystic lymphatic tumors known as lymphangioleiomyomas and angiomyolipomas commonly affecting the kidneys. Patients presenting initial symptoms consist of dyspnea, spontaneous pneumothorax or less commonly cough hemoptysis or chylous effusions. Radiographic findings demonstrate diffuse bilateral distribution of thin-walled pulmonary cystic changes on CT of the chest. We present an atypical case of a patient with tuberous sclerosis complex, presenting with unilateral pulmonary lymphangioleiomyomatosis.

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Cite the article

Costa J, Thomashow B, Rosenblatt MP, D'Ovidio F. Atypical Case of Pulmonary Lymphangioleiomyomatosis. Clin Surg. 2021; 6: 3067.