Management of Hemostasis in Acute Aortic Dissection Type A Diagnosed with Von Willebrand Disease - Case Report

Cavolli Raif1*, Cavolli Viola1 , Sotiraq Lako2 , Memishaj Sabian1 and Uymaz Baris2

1 Department of Cardiac Surgery, University Clinical Center of Kosova, Kosovo 2 Department of Cardiac Surgery, American Hospital, Albania

^*Correspondance to: Raif Cavolli 

 PDF  Full Text DOI: 10.25107/2474-1647.3030

Abstract

Abstract Background: Von Willebrand Disease (VWD), the most common hereditary bleeding disorder, arises from quantitative or qualitative defect of VWF. There are only a few report of patient undergoing cardiac surgery with VWD. Case Presentation: A patient knows as type 1 VWD was diagnosed with Type A Aortic Dissection. He was treated prior to and after surgery with cryoprecipitate preventing coagulopathy in the absence of the von Willebrand/factor VIII concentrate. Conclusion: Despite the absence of von Willebrand/factor VIII concentrate in our country the use of cryoprecipitate allowed our patient to undergo the aortic surgery without any complication.

Keywords

Von Willebrand disease; Aortic dissection; Bleeding

Cite the article

Raif C, Viola C, Lako S, Sabian M, Baris U. Management of Hemostasis in Acute Aortic Dissection Type A Diagnosed with Von Willebrand Disease - Case Report. Clin Surg. 2021; 6: 3030..