Ulnar Hemimelia with Humero-Radial Synostosis and Oligodactyly: A Rarity and Review of Literature

Aditya K Aggarwal*, Karmesh Kumar Shahnawaz Khan and Ankush Sood

Department of Orthopedic Surgery, Post Graduate Institute of Medical Education & Research, India

^*Correspondance to: Aditya K Aggarwal 

 PDF  Full Text DOI: 10.25107/2474-1647.3000

Abstract

Ulnar hemimelia is a very rare condition. In most of the cases, it goes unreported due to death of fetus in-utero owing to other anomalies during organogenesis. The association of ulnar hemimelia with humero-radial synostosis and oligodactyly makes our case very rare and unusual. It presents as shortening of upper limb, rigid elbow, ulnar clubbing and coalition or absence of metacarpals. A rare case of ulnar hemimelia with humeroradial synostosis and absence of one metacarpal on ulnar side is presented in an 8 months old female child. Detailed review of literature Management of this condition is quite individualized. The management of this condition involves early physiotherapy followed by multiple soft tissue release if required. Parental counseling is of utmost importance while dealing with such conditions.

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Cite the article

Aggarwal AK, Khan KKS, Sood A. Ulnar Hemimelia with Humero-Radial Synostosis and Oligodactyly: A Rarity and Review of Literature. Clin Surg. 2020; 5: 3000..