Surgical Management of an Intrathoracic Desmoid Tumor: A Rare Presentation

Santivanez JJ1*, Diaz A2 , Jimenez A3 and Garcia-Herreros LG

1 Department of Surgery, Fundacion Santa Fe de Bogota, Colombia 2 Department of Thoracic Surgery, Universidad El Bosque, Bogota, Colombia 3 Department of Thoracic Surgery, Fundacion Santa Fe de Bogota, Colombia

^*Correspondance to: Juan Jose Santivanez 

 PDF  Full Text DOI: 10.25107/2474-1647.2990

Abstract

Desmoid tumor is a rare connective tissue tumor, accounting for approximately 3.5% of connective tissue tumors and 0.3% of all solid tumors. It can originate in any part of the body; however, we find them more frequently in extremities, thorax and abdomen. True intrathoracic desmoid tumors however (arise within the thoracic cavity) are remarkably rare. The main problem is the ability to continue growing more than in another location and the high relapse rates of this tumor. Adequate surgical resection with negative margins is the treatment of choice; however in cases of positive margins, advanced stages of the disease, or in unresectable locations, other therapies are being used. We present a case of a left parietal pleural 22 cm desmoid tumor that occupied the entire left pleural space with severe adhesions, and complete collapse of the lower lobe.

Keywords

Desmoid tumor; Chest wall; Intrathoracic; Intrapleural

Cite the article

Santivanez JJ, Diaz A, Jimenez A, Garcia-Herreros LG. Surgical Management of an Intrathoracic Desmoid Tumor: A Rare Presentation. Clin Surg. 2020; 5: 2990.