Primary Intracranial Intra Axial Ewing's Sarcoma: A Rare Case Report with Unusual Location & Short Review on Literature

Naresh Panwar, Somnath Sharma and Devendra K Purohit

Department of Neurosurgery, SMS Medical College, Jaipur, India

^*Correspondance to: Naresh Panwar 

 PDF  Full Text DOI: 10.25107/2474-1647.1946

Abstract

Ewing's Sarcoma (ES) is one of the frequently seen and catastrophic malignancies of childhood incriminate long bones and soft tissue. As far intracranial manifestations of the disease are concerned, which are extremely rare in reality, Most of the reported cases of ES involving Central Nervous System (CNS) represent secondary metastases from extra cranial sites. Although there are very few cases reported of primary Ewing's sarcoma of cranium. A search of the literature suggests that these tumors are mostly dural based or extra axial mimicking as meningeal tumors and most commonly seen in younger population. We present the clinical, radiologic and pathologic findings of an primary intracranial intra axial Ewing sarcoma/pPNET in a 42-year-old male located in left Parieto-occipital sub cortical zone, and radiologically presenting as Glioblastoma Multiforme (GBM).This site is highly unusual for intra axial ES, and to the best of authors knowledge this is third case of intra-axial intra parenchymal ES/pPNET.

Keywords

Ewing sarcoma/peripheral primitive neuroectodermal tumor; Primary intracranial intra-axial; Central nervous system

Cite the article

Panwar N, Sharma S, Purohit DK. Primary Intracranial Intra Axial Ewing's Sarcoma: A Rare Case Report with Unusual Location & Short Review on Literature. Clin Surg. 2018; 3: 1946.