Klippel-Feil Syndrome: When Using Fiberoptic Bronchoscopy Guide, a Case Report

Federico Bizzarri, Andriy Dralov, Antonio Segreto, Cantarano Maria Sole, Paolo De Siena, Di Pinto Luca, Stefano Congiu, Caren Van Doorn and Luisa Carin

Department of Science and Medical Surgical Biotechnologies, Cardiac Surgery Unit, “Sapienza” University of Roma, Italy Pediatric Cardiac Surgery Unit, Leeds General Infirmary, UK
Department of Cardiac Surgery, San Matteo Hospital, Italy

^*Correspondance to: Luisa Carini 

 PDF  Full Text DOI: 10.25107/2474-1647.1841

Abstract

Klippel-Feil syndrome is a rare disease with congenital musculoskeletal condition characterized by faulty segmentation of cervical vertebrae and consists of cervical vertebra fusions with limitation of head movements, short neck and low posterior hairline. In several cases the syndrome is associated with cardiovascular malformations. Patients affected by Klippel-Feil syndrome could be an anesthetic challenge, not only during cardiac surgery. We are presenting a case of Klippel-Feil Syndrome in an adult patient, who was operated on for a pulmonary valve insufficiency in a previously corrected Tetralogy of Fallot Syndrome. We are going to discuss the features of this rare syndrome.

Keywords

Klippel-Feil syndrome; Anesthesia; Cardiac surgery; Tetralogy of fallot; Intubation; Vertebral fusion

Cite the article

Bizzarri F, Dralov A, Segreto A, Sole CM, De Siena P, Luca DP, et al. Klippel-Feil Syndrome: When Using Fiberoptic Bronchoscopy Guide, a Case Report. Clin Surg. 2017; 2: 1841.