Persistent Mullerian Duct Syndrome (PMDS) with Testicular Seminoma

Ray MD, Kumar S, Bhoriwal S, Mishra A, Padmanaban N and Gowda SM

Department of Surgical Oncology, All India Institute of Medical Sciences, India

^*Correspondance to: Manoj Gowda S 

 PDF  Full Text DOI: 10.25107/2474-1647.1119

Abstract

Introduction: Persistent mullerian duct syndrome is a rare disorder in 46, XY male with persistent mullerian duct structures (uterus, fallopian tubes and vagina). 15% of cryptorchid testes will have malignant transformation.Case Report: A 39 year old male presented with pain abdomen since 1 year. CT scan showed a mass in rectovesical pouch and mesentery. Biopsy was seminoma testis. AFP level was normal. After 3 cycles of chemotherapy (BEP) excision of both masses done. Pathological examination showed uterus and fallopian tube with leidig cell hyperplasia in right testis.Conclusion: Surgeons and pathologists should be aware of such a diagnosis in any patient who presents with undescended testis and mass behind urinary bladder in imaging.

Keywords

Persistent mullerian duct syndrome; Seminoma; Cryptorchidism

Cite the article

Ray MD, Kumar S, Bhoriwal S, Mishra A, Padmanaban N, Gowda SM. Persistent Mullerian Duct Syndrome (PMDS) with Testicular Seminoma. Clin Surg. 2016; 1: 1119.