Department of Pediatrics, Erciyes University, TurkeyFulltext PDF
Introduction: Myxomas; although they are the most common primary cardiac tumors in the adults; they are very rare in pediatric age group. There is limited data in the literature. In this report we aimed to present an interesting neonatal case operated for the myxoma obstructing the right ventricular outflow tract. Case: Five days-old full-term male infant weighted 3700 gr was referred to our center for the heart murmur. Transthoracic echocardiogram revealed a mass in the right ventricle sized 13.5 mm × 8 mm. It was seen that the mass was prolapsing in Right Ventricular Outflow Tract (RVOT) in each systole and causing an obstruction. We have measured 60 mmHg pressure gradients in RVOT. Successful excision of the tumor was done without any complications. Pathological investigation revealed that the excised tumor was a myxoma.
Discussion: Myxomas usually arise from the right atrium or the left ventricular cavity. The most interesting feature of our case that myxoma originated from RV not from atria. In the literature we have found only three reports of neonatal right ventricular myxomas therefore our case is the fourth one. Most neonatal cardiac tumors are rhabdomyomas that regress by time. Myxomas are rare in pediatric age group, only sporadic cases were reported. They are benign tumors however, if they increase in size and cause an obstruction in outflow tract like our case, should be treated by surgical excision.
Pamukcu O. A Neonatal Myxoma, Obstructing Right Ventricular Outflow Tract. Clin Surg. 2019; 4: 2437.