Federico Bizzarri1, Andriy Dralov1, Antonio Segreto1, Cantarano Maria Sole1, Paolo De Siena3, Di Pinto Luca1, Stefano Congiu2, Caren Van Doorn2 and Luisa Carini1*
1Department of Science and Medical Surgical Biotechnologies, Cardiac Surgery Unit, “Sapienza” University of Roma, Italy 2Pediatric Cardiac Surgery Unit, Leeds General Infirmary, UK
3Department of Cardiac Surgery, San Matteo Hospital, Italy
Klippel-Feil syndrome is a rare disease with congenital musculoskeletal condition characterized by faulty segmentation of cervical vertebrae and consists of cervical vertebra fusions with limitation of head movements, short neck and low posterior hairline. In several cases the syndrome is associated with cardiovascular malformations. Patients affected by Klippel-Feil syndrome could be an anesthetic challenge, not only during cardiac surgery. We are presenting a case of Klippel-Feil Syndrome in an adult patient, who was operated on for a pulmonary valve insufficiency in a previously corrected Tetralogy of Fallot Syndrome. We are going to discuss the features of this rare syndrome.
Klippel-Feil syndrome; Anesthesia; Cardiac surgery; Tetralogy of fallot; Intubation; Vertebral fusion
Bizzarri F, Dralov A, Segreto A, Sole CM, De Siena P, Luca DP, et al. Klippel-Feil Syndrome: When Using Fiberoptic Bronchoscopy Guide, a Case Report. Clin Surg. 2017; 2: 1841.