Mihaylov V*, Kostadinov R, Vasilevski I, Takorov I, Simonova M, Katzarov K, Odiseeva E and Vladov N
Department of Transplant Surgery, Military Medical Academy, BulgariaFulltext PDF
Hepatic epithelioidhemangioendothelioma (HEHE) is a rare vascular tumor of the liver, with less than 500 cases reported worldwide. It has indolent course and often presents with unspecific symptoms. Unlike other primary liver tumors, it does not arise in the background of chronic liver disease. The definitive diagnosis is difficult and often necessitates percutaneous liver biopsy. Another feature of HEHE is its variable and unpredictable prognosis. Due to the rarity of this condition, currently there is no accepted treatment approach. Excellent results are achieved through the surgical modalities-liver resection (LR) and liver transplantation (LT), with high survival rates and disease free survival (DFS). Other therapeutic options include chemo/radiotherapy regiments and transcatheter arterial chemoembolization (TACE). We present a case report of 33 years old male with multiple bilobar hepatic epithelioid hemangioendothelioma who underwent orthotopic liver transplantation with excellent long-term outcome.
Mihaylov V, Kostadinov R, Vasilevski I, Takorov I, Simonova M, Katzarov K, et al. Liver Transplantation for Hepatic Epithelioid Hemangioendothelioma Case Report and Review of the Literature. Clin Surg. 2017; 2: 1322.